Acute Shock in an Ambiguous Child

Authors

  • Pranab Kumar Sahana Associate Professor, Department of Endocrinology, N.R.S. Medical College & Hospital, Kolkata-700014, West Bengal
  • Nilanjan Sengupta Associate Professor & Head, Department of Endocrinology, N.R.S. Medical College & Hospital, Kolkata-700014, West Bengal
  • Mukut Roy Post Doctoral Trainee (Endocrinology), Department of Endocrinology, N.R.S. Medical College & Hospital, Kolkata-700014, West Bengal
  • Ashish Deshmukh Post Doctoral Trainee (Endocrinology), Department of Endocrinology, N.R.S. Medical College & Hospital, Kolkata-700014, West Bengal
  • Ranehn Dasgupta Professor & Ex-Head Department of Endocrinology, N.R.S. Medical College & Hospital, Kolkata-700014, West Bengal

DOI:

https://doi.org/10.3329/bccj.v2i1.19957

Keywords:

Congenital adrenal hyperplasia, Ambiguous genitalia, Salt wasting crisis, Glucocorticoid, Fludrocortisone

Abstract

Patients with congenital adrenal hyperplasia (CAH) usually presents with varied manifestations. In female, it can manifest as ambiguous genitalia, salt wasting crisis or androgen excess in puberty depending on the severity of enzyme deficiency. Here, we report a four and half year old girl who developed salt wasting crisis in the neonatal period. Prompt diagnosis and immediate glucocorticoid and fludrocortisone replacement saved her life. High index of suspicion is needed to diagnose CAH and continued replacement of glucocorticoid and mineralocorticoid is needed to suppress virilization of the female child and prevent further crises.

Bangladesh Crit Care J March 2014; 2 (1): 38-39

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Published

2014-08-11

How to Cite

Sahana, P. K., Sengupta, N., Roy, M., Deshmukh, A., & Dasgupta, R. (2014). Acute Shock in an Ambiguous Child. Bangladesh Critical Care Journal, 2(1), 38–39. https://doi.org/10.3329/bccj.v2i1.19957

Issue

Vol. 2 No. 1 (2014)

Section

Case Reports

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