Electro Clinical Profiles of Motor Neuron Disease and Atypical Motor Neuron Disorders: A Case Series

Authors

  • Bithi Debnath Assistant Professor, Department of Paediatric Neurology, National Institute of Neurosciences and Hospital, Dhaka
  • Humaira Rafiqa Quaderi Assistant Professor, Department of Pediatric Neurosciences, Dhaka Shishu Hospital, Dhaka
  • Nazmul Haque Assistant Professor, Department of Paediatric Neurology, National Institute of Neurosciences and Hospital, Dhaka
  • AFM Al Masum Khan Medical Officer, Department of Interventional Neurology, National Institute of Neurosciences and Hospital, Dhaka
  • Meera Momtaz Sabeka Registrar, Department of Neurophysiology, National Institute of Neurosciences and Hospital, Dhaka
  • Md Ferdous Mian Assistant Professor, Department of Neurology, National Institute of Neurosciences and Hospital, Dhaka
  • Md Nahidul Islam Assistant Professor, Department of Neurology, National Institute of Neurosciences and Hospital, Dhaka
  • Md Enayet Hussain Assistant Professor, Department of Neurology, National Institute of Neurosciences and Hospital, Dhaka
  • Rajib Nayan Chowdhury Associated Professor & Head, Department of Neurophysiology, National Institute of Neurosciences and Hospital, Dhaka

DOI:

https://doi.org/10.3329/jninb.v3i1.36274

Keywords:

Motor Neuron Disease, MND, Atypical Motor Neuron Disorders, Electrodiagnostic test, EDX, Amyotrophic lateral sclerosis, ALS

Abstract

Amyotrophic lateral sclerosis (ALS) is the commonest MND phenotype. Although many of the atypical motor neuron disorders share some features with ALS, they often can be distinguished by their clinical and electrophysiologic characteristics. Here we present five different cases with varied clinical findings. All the patients were referred from outpatient department to neurophysiology laboratory where electrodiagnostic (EDX) correlations helped to come to a conclusion. The nerve conduction study protocol for a suspected atypi¬cal motor neuron disorder is the same as that for ALS. Akin to the nerve conduction studies, the EMG evaluation of patients with suspected atypical motor neuron disorders is similar to that of ALS. An extensive study is indicated, often of all four limbs, the paraspinal muscles, and the bulbar muscles to reach a possible diagnosis. History, clinical findings and electrophysiological correlation often help to differentiate these atypical motor neuron disorders. Correct diagnosis is needed for further evaluation and prognosis. In this case series five (5) cases have described who are referred from outpatient department to neurophysiology laboratory for electrodiagnostic (EDX) correlations.

Journal of National Institute of Neurosciences Bangladesh, 2017;3(1): 57-61

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Published

2018-04-06

How to Cite

Debnath, B., Quaderi, H. R., Haque, N., Khan, A. A. M., Sabeka, M. M., Mian, M. F., Islam, M. N., Hussain, M. E., & Chowdhury, R. N. (2018). Electro Clinical Profiles of Motor Neuron Disease and Atypical Motor Neuron Disorders: A Case Series. Journal of National Institute of Neurosciences Bangladesh, 3(1), 57–61. https://doi.org/10.3329/jninb.v3i1.36274

Issue

Vol. 3 No. 1 (2017)

Section

Case Reports

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