Journal of Paediatric Surgeons of Bangladesh The official journal of the Association of Paediatric Surgeons of Bangladesh (APSB). Full text articles available. Association of Paediatric Surgeons of Bangladesh en-US Journal of Paediatric Surgeons of Bangladesh 2077-7469 <p>Authors of articles published in <em>JPSB </em>retain the copyright of their articles and are free to reproduce and disseminate their work. A Copyright and License Agreement – signed and dated by the corresponding author on behalf of all authors – must be submitted with each manuscript submission.</p> Counselling of Parents, attendants, guardians in dealing of Paediatic Surgical Patients <p>Abstract not available</p><p>J. Paediatr. Surg. Bangladesh <strong>6</strong>(2): 32, 2015 (July)</p> Kazi Habibur Rahman Copyright (c) 2016 Kazi Habibur Rahman 2016-05-15 2016-05-15 6 2 32 32 10.3329/jpsb.v6i2.27746 Spinal Primitive Neuroectodermal Tumor in Children – A rare case report and literature review <p>Primitive neuroectodectodermal tumor is a rare tumor in childhood. It is aggressive childhood malignancies and offer a significant challenge to treatment. An eleven year old female baby presented with fever, pain and neurologic manifestation. Initialy it was diagnose as TB vertebrae and treated accordingly but no improvment rather new metastatic swelling appear after few days. Diagnosis was made by MRI and local tissue biopsy and immunohistohistochemistry. As it is rare and highly invasssive malignancy with poor out come the case was presented along with literature review.</p><p>J. Paediatr. Surg. Bangladesh <strong>6</strong>(2): 64-67, 2015 (July)</p> AKM Amirul Morshed Shahnoor Islam Sayeeda Anwar Copyright (c) 2016 AKM Amirul Morshed, Shahnoor Islam, Sayeeda Anwar 2016-05-15 2016-05-15 6 2 64 67 10.3329/jpsb.v6i2.27751 Three Years Experience of Inguinal Hernia in Children in BSMMU <p><strong>Objective:</strong> The aim of this study is to evaluate the management of inguinal hernias in children as a day case surgery in elective basis.</p><p><strong>Methods:</strong> From July 2011 to June 2014, 141 infants and children with inguinal hernias were seen, operated on, and followed up as outpatient procedure in the Department of Paediatric Surgery of Bangabandhu Sheikh Mujib Medical University Dhaka, Bangladesh (BSMMU) Age, sex, side of hernia, presence of an associated hydrocele/ undescended testes/ VPshunt, occurrence of contralateral hernia, clinical aspects of these patients, type of surgery, mortality, and mobidity were studied</p><p><strong>Results:</strong> The ages ranged from 2months to 14 years (mean age, 6.28 years) with a male-to female ratio of 3:1. There were 59.6% right, 34.8% left, and 5.7% bilateral hernias (all are indirect variety).The most common associated anomaly was hydrocele in 29(20.8%)patients, undescended testis in 9(6.5%) patients and in 4(2.8%) patients had ventriculoperitoneal shunt. The content of the hernial sac in 56(39.7%) patients were omentum and next were intestine in 30(21.3%) patients. Overall, there were 13 (9.2%) sliding hernias. Among them in five case of boys four (80%) patients contents were cecum and one (20%) patient was sigmoid colon. In case of girls, contents were ovaries in all eight patients. Contralateral groin exploration was not done of any patients at the initial hernia repair. There were recurrences in 2(1.4%) patients, 13(9%) patients developed wound infections, and 21(15%) patients had scrotal haematocele. There were no postoperative deaths. A contralateral hernia developed in three (2%) children within one year after the initial repair.</p><p><strong>Conclusions:</strong> Inguinal hernia is a common surgical condition in children. Elective surgery is associated with minimal morbidity. A routine contralateral groin exploration is not done at the initial hernia repair</p><p>J. Paediatr. Surg. Bangladesh <strong>6</strong>(2): 34-38, 2015 (July)</p> Shoheli Alam KM Didarul Islam Abu Saleh Md Oli Ullah Md Tosaddeque Hossain Siddiqui Md Ruhul Amin Copyright (c) 2016 Shoheli Alam, KM Didarul Islam, Abu Saleh Md Oli Ullah, Md Tosaddeque Hossain Siddiqui, Md Ruhul Amin 2016-05-15 2016-05-15 6 2 34 38 10.3329/jpsb.v6i2.27747 Outcome of Partial Splenectomy for Hypersplenism in Children with Thalassemia <p><strong>Background:</strong> Total splenectomy, exposes children to the high risk of overwhelming postsplenectomy infections (OPSI). To avoid these adverse consequences, partial splenectomy has long been practiced for thalasseemia in children. It has been reported that the partial splenectomy keeps the child immunologically competent, hematologically stable with minimum blood transfusion and makes their life more comfortable in comparison to total splenectomy.</p><p><strong>Objectives:</strong> To compare the results of partial and total splenectomy.</p><p><strong>Methodology:</strong> This prospective interventional comperative study was done in the department of Pediatric Surgery, BSMMU from 2010 to 2012. Children who underwent partial splenectomy were considered as the case and who underwent total splenectomy as the control. Number of blood (RCC) transfusions (ml/ kg/year), Peripheral blood film (Hb%, WBC count, platelet count, Howell-Jolly body, serum bilirubin), volume of liver (ml), volume of spleen (ml), number of OPSI case, were compared between the case and control groups both pre and postoperatively.</p><p><strong>Results:</strong> Postsplenectomy blood transfusion requirement is comparatively more decreased in control group than case group. The inter group difference at 6 month is significant (p= 0.004). Peripheral blood pictures are improved in both groups. Post splenectomy hemoglobin level was increased in both groups but it was maintained at a more static fashion in control group than case group (P = 0.114). Howell-jolly body in the partial splenectomy group disappeared almost completely at month 6, while the same inclusion body in the total splenectomy group appeared in all the children (p= 0.001). There was no postsplenectomy infection in case group while two found in control group. After partial splenectomy the residual volume of the spleen was gradually increasing. The increase in volume of the liver was notably greater in the total splenectomy group than that in the partial splenectomy group (p&lt; 0.05).</p><p><strong>Conclusion:</strong> Partial splenectomy in patients with ²-thalassemia is effective in controlling hemolysis, improving peripheral blood picture while preserving the residual splenic phagocytic and immune function.</p><p>J. Paediatr. Surg. Bangladesh <strong>6</strong>(2): 39-46, 2015 (July)</p> Mizanur Rahman Susankar Kumar Mondal Amin Lutful Kabir Md Ruhul Amin Matiur Rahman Copyright (c) 2016 Mizanur Rahman, Susankar Kumar Mondal, Amin Lutful Kabir, Md Ruhul Amin, Matiur Rahman 2016-05-15 2016-05-15 6 2 39 46 10.3329/jpsb.v6i2.27748 Abdominal Ultrasonography and Radiography Diagnosis in Preterm Necrotizing Enterocolitis <p><strong>Introduction<em>: </em></strong>Necrotizing enterocolitis (NEC) is a major cause of neonatal morbidity and mortality. To explore whether abdominal ultrasound (AUS) provide additional information over plain radiography in cases of necrotizing enterocolitis (NEC).</p><p><strong>Materials &amp; Methods<em>: </em></strong>This study is a prospective study of 30 premature neonates with NEC in our neonatal intensive care unit between September 2013 and November 2014. Fifteen premature control neonates were also included in the study.</p><p><strong>Results:</strong><em> </em>Patients were classified into two groups: the first group with suspected NEC (stage I) (n = 14) and the second with definite NEC (stage II or III) (n = 16). In group I abdominal ultrasound (AUS) revealed intramural air (n = 9) and portal venous gas (PVG) (n = 1) while plain radiography showed only gaseous distension. In group II, intramural air (n = 10), PVG (n = 2), free fluid (n = 6) focal fluid (n = 1) and free air (n = 6) detected by AUS compared to pneumatosis intestinalis (PI) (n = 2) PVG (n = 1) and free air (n = 5) by plain radiography. Additionally bowel wall thinning was detected in 2 neonates of group I and 3 of group II.</p><p><strong>Conclusion:</strong><em> </em>Our results suggest AUS to be superior to plain radiography in early detection of complication as intestinal perforation by eliciting PVG and fluid collection and so early surgical management. Therefore this may decrease morbidity and mortality rates.</p><p>J. Paediatr. Surg. Bangladesh <strong>6</strong>(2): 47-53, 2015 (July)</p> S Tuya Ch Battulga TS Tsogtsolmaa M Tumennasan N Davaatseren Kaniz Hasina Copyright (c) 2016 S Tuya, Ch Battulga, TS Tsogtsolmaa, M Tumennasan, N Davaatseren, Kaniz Hasina 2016-05-15 2016-05-15 6 2 47 53 10.3329/jpsb.v6i2.27749 Hemophilia in Children <p>Hemophilia is the most common serious congenital coagulation factor deficiencies. The prevalence of hemophilia is estimated to be about 1:10,000 birth and that of the severe form of the disease to be about 6% per 1,00,000 population. The most pathetic part of this disease is that even medical personnel are sometimes not familiar with its diagnosis and management. There is obviously a need to establish facilities and treatment options that will help the patient with hemophilia to manage their life with ease. As this is a genetic disorder no complete cure is possible as of now. The only available treatment option is the infusion of factors and some adjuvant therapies depending upon the bleeding conditions .Hemophilia, if not properly managed, can lead to chronic disease and lifelong disabilities. The challenges and issues in infants/young children are different from those in older children and adults although episodes of bleeding still predominate as the diagnostic trigger. Currently, inhibitor development is a challenging complication of pediatric hemophilia and prophylaxis is emerging as the optimal preventive care strategy. In this section we will review some important aspects of hemophilia in children including early prophylaxis, current evidence relating to inhibitor development.</p><p>J. Paediatr. Surg. Bangladesh <strong>6</strong>(2): 54-63, 2015 (July)</p> Shahnoor Islam AKM Amirul Morshed Zohora Jameela Khan Copyright (c) 2016 Shahnoor Islam, AKM Amirul Morshed, Zohora Jameela Khan 2016-05-15 2016-05-15 6 2 54 63 10.3329/jpsb.v6i2.27750