Gorlin Goltz Syndrome- A Rare Disease Reported In Bangladesh

Authors

  • Nafisa Afroze Lecturer (Oral and Maxillofacial Surgery), Update Dental College and Hospital, Dhaka, Bangladesh
  • ASM Ariful Islam Assistant Professor and Head (Oral and Maxillofacial Surgery), Update Dental College & Hospital, Dhaka, Bangladesh
  • Md Shofiqul Islam Lecturer (Oral and Maxillofacial Surgery), Update Dental College & Hospital, Dhaka, Bangladesh
  • Jeyasmin Akter Lipi Lecturer (Oral And Maxillofacial Surgery), Update Dental College & Hospital, Dhaka, Bangladesh

DOI:

https://doi.org/10.3329/updcj.v12i2.61430

Keywords:

Gorlin Goltz Syndrome, Odontogenic Keratocyst, PTCH Gene

Abstract

Gorlin-Goltz syndrome is an infrequent multisystemic disease with an autosomal dominant trait with complete penetrance and various expressivity. Gorlin Goltz Syndrome is a rare autosomal characterized by an increased predisposition to basal cell carcinoma and associated with multiorgan anomalies having a high level of penetrance. We report here a 60-year-old patient with positive findings of Gorlin-Goltz Syndrome.The following report emphasizes the identification of all the essential clinical diagnostic criteria ,radiological manifestations, and possible genetic tests to be performed for setting up an adequate treatment plan.

Update Dent. Coll. j: 2022; 12(2): 32-36

 

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Published

2022-10-10

How to Cite

Afroze, N. ., Islam, A. A., Islam, M. S., & Lipi, J. A. (2022). Gorlin Goltz Syndrome- A Rare Disease Reported In Bangladesh. Update Dental College Journal, 12(2), 32–36. https://doi.org/10.3329/updcj.v12i2.61430

Issue

Section

Case Reports