A Case Report of Hallervorden-Spatz Disease with Classical Magnetic Resonance Imaging Feature

Authors

  • Shahida Bulbul Department of Neurology, Bangabandhu Sheikh Mujib Medical University, Dhaka
  • Md. Shahidullah Department of Neurology, Bangabandhu Sheikh Mujib Medical University, Dhaka
  • Sujan Saha Department of Neurology, National Institute of Neurosciences & Hospital, Dhaka
  • Tahira Zannat Department of Neurology, Bangabandhu Sheikh Mujib Medical University, Dhaka
  • Rajib Das Department of Neurology, Bangabandhu Sheikh Mujib Medical University, Dhaka
  • Salman Rafat Department of Gastroenterology, Bangabandhu Sheikh Mujib Medical University, Dhaka
  • Hasan Mahmud Department of Anasthesia, Bangabandhu Sheikh Mujib Medical University, Dhaka
  • Md. Abdullah Al Muzahid Department of Neurology, Bangabandhu Sheikh Mujib Medical University, Dhaka
  • Mehedi Hasan Department of Neurology, Bangabandhu Sheikh Mujib Medical University, Dhaka
  • Ashish Chowdhury Department of Neurology, Bangabandhu Sheikh Mujib Medical University, Dhaka

DOI:

https://doi.org/10.3329/bjn.v39i1.88431

Keywords:

Hallervorden-Spatz disease, Eye of the tiger sign

Abstract

Hallervorden-Spatz disease is a rare neurometabolic disorder characterized by iron accumulation in the brain, manifesting with extrapyramidal symptoms, psychosis, dementia, and retinal degeneration. This report presents a case exhibiting dystonia, retinitis pigmentosa, and psychotic symptoms, accompanied by classical magnetic resonance imaging (MRI) feature. MRI of brain of two asymptomatic siblings of index case also demonstrated the characteristic “eye of the tiger” sign.

Downloads

Download data is not yet available.
Abstract
11
PDF
2

Downloads

Published

2026-03-15

How to Cite

Bulbul, S., Md. Shahidullah, Sujan Saha, Tahira Zannat, Rajib Das, Salman Rafat, … Ashish Chowdhury. (2026). A Case Report of Hallervorden-Spatz Disease with Classical Magnetic Resonance Imaging Feature. Bangladesh Journal of Neuroscience, 39(1), 45–47. https://doi.org/10.3329/bjn.v39i1.88431

Issue

Vol. 39 No. 1 (2023)

Section

Case Reports

License

Copyright (c) 2026 Shahida Bulbul, Md. Shahidullah, Sujan Saha, Tahira Zannat, Rajib Das, Salman Rafat, Hasan Mahmud, Md. Abdullah Al Muzahid, Mehedi Hasan, Ashish Chowdhury

Creative Commons License

This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International License.

Most read articles by the same author(s)

1 > >>