Cleidocranial Dysplasia of a 13-year-old Bangladeshi Girl: A Rare Case Report

Authors

  • Sufia Nasrin Rita Head, Department of Orthodontics, Sapporo Dental College and Consultant, Square Hospitals Ltd, Dhaka, Bangladesh
  • Muhammad Mahdee Hasan Assistant Professor, Department of Orthodontics, Sapporo Dental College, Dhaka, Bangladesh
  • Nurul Amin Head, Department of oral & maxillofacial surgery, Sapporo Dental College, Dhaka, Bangladesh
  • SM Anwar Sadat Associate Professor, Department of Oral & Maxillofacial Surgery, Dhaka Dental College and Consultant, Square Hospitals Ltd, Dhaka, Bangladesh

DOI:

https://doi.org/10.3329/jbcps.v38i4.48982

Keywords:

Autosomal InheritanceCleidocranial Dysplasia, Delayed Eruption,Supernumerary Teeth

Abstract

Cleidocranial dysplasia (CCD) is an uncommon autosomal inheritant congenital skeletal defect that primarily affects the bones and teeth, and shows an autosomal inheritance. A 13-year-old Bangladeshi girl presented with delayed eruption of the permanent anterior teeth. She was short-statured, well-oriented young girl with narrow, drooped shoulders, malformed or absent clavicles, brachycephalic head with frontal and parietal bossing, hypoplasticzygomatic bones, bulging calvarium, and depressed nasal bridge with a broad alar base. Intraoral examination revealed persistence of the primary dentition, delayed eruption of the permanent teeth, an Angle class III malocclusion, negative overjet, bilateral posterior crossbite. This rarecase of CCD is so far the first case from Bangladesh to be documented in perspective to dental surgery and orthodontics.

J Bangladesh Coll Phys Surg 2020; 38(4): 213-217

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Published

2020-09-08

How to Cite

Rita, S. N., Hasan, M. M., Amin, N., & Sadat, S. A. (2020). Cleidocranial Dysplasia of a 13-year-old Bangladeshi Girl: A Rare Case Report. Journal of Bangladesh College of Physicians and Surgeons, 38(4), 213–217. https://doi.org/10.3329/jbcps.v38i4.48982

Issue

Section

Case Reports