Atypical ‘Granulomatosis with Polyangiitis’ Presenting with Epistaxis

Authors

  • Sumaiya Akter Asstt. Registrar of Medicine, Popular Medical College, Dhaka, Bangladesh
  • HAM Nazmul Ahasan Professor of Medicine, Popular Medical College, Dhaka, Bangladesh
  • Quazi Tarikul Islam Professor of Medicine, Popular Medical College, Dhaka, Bangladesh

DOI:

https://doi.org/10.3329/jom.v22i1.51400

Keywords:

Atypical Wegener’s granulomatosis, granulomatosis with polyangiitis, limited GPA

Abstract

Granulomatosis with polyangiitis (GPA) is a systemic necrotizing vasculitis involving small and mediumsized blood vessels and granulomatous inflammation of upper and lower respiratory systems and/or renal system. In the limited form of GPA, there is no systemic involvement of disease with sparing of kidneys. Herein, we report a case of 37-year-old male who was diagnosed as ethmoidal polyposis clinically. Ethmoidal tissue biopsy granulomatous angiitis. Diagnosis of GPA was made which was substantiated by antineutrophil cytoplasmic antibody (ANCA) positivity. This was a case of GPA involving only upper respiratory system. The early diagnosis and initiation of treatment are critical for improved survival of patients with GPA. Tissue biopsy is necessary for the diagnosis of GPA.

J MEDICINE JAN 2021; 22 (1) : 81-83

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Published

2021-01-14

How to Cite

Akter, S., Ahasan, H. N., & Islam, Q. T. (2021). Atypical ‘Granulomatosis with Polyangiitis’ Presenting with Epistaxis. Journal of Medicine, 22(1), 81–83. https://doi.org/10.3329/jom.v22i1.51400

Issue

Vol. 22 No. 1 (2021)

Section

Case Reports

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