Dandy–Walker Malformation Presenting with Refractory Seizures and Unilateral Pan-ophthalmitis in Infancy: Successful Management with Dual Ventricular Shunting

Authors

  • Saumitra Sarkar Professor, Department of Neurosurgery, Sylhet MAG Osmani Medical College Hospital, Sylhet & Visiting Consultant Neurosurgeon, BGB Hospital, Dhaka, Bangladesh
  • Shuvro Saha Medical officer, Department of Neurosurgery, Dhaka Medical College Hospital, Dhaka, Bangladesh
  • Saumik Sarkar Resident Medical officer, Department of Intensive Care Unit, Popular Medical College Hospital, Dhaka, Bangladesh
  • Md Shahadat Hossain Sarker Medical Officer, Department of Neurosurgery, Dhaka Medical College Hospital, Dhaka, Bangladesh
  • Avijit Dey Registrar, Department of Neurosurgery, Shaheed Suhrawardy Medical College Hospital, Dhaka, Bangladesh
  • Anindya Das Gupta Medical Officer, Department of Neurosurgery, National Institute of Neuroscience Hospital, Dhaka, Bangladesh

Keywords:

Dandy–Walker malformation, Congenital hydrocephalus, Dual ventriculoperitoneal shunt, Y-connector shunt system, Infantile seizures, Posterior fossa malformation

Abstract

Dandy–Walker malformation (DWM) is a congenital posterior fossa anomaly frequently associated with hydrocephalus and neurodevelopmental impairment. We report an unusual presentation of DWM in an infant with recurrent convulsions and unilateral pan-ophthalmitis leading to loss of  vision, managed successfully with emergency dual ventriculoperitoneal shunting using a Y-connector. At 27 months of age, the child demonstrates normal neurodevelopment with seizure control on tapering antiepileptic therapy.

J Shaheed Suhrawardy Med Coll 2025; 17(1): 107-110

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Published

2026-07-30

How to Cite

Saumitra Sarkar, Shuvro Saha, Saumik Sarkar, Md Shahadat Hossain Sarker, Avijit Dey, & Anindya Das Gupta. (2026). Dandy–Walker Malformation Presenting with Refractory Seizures and Unilateral Pan-ophthalmitis in Infancy: Successful Management with Dual Ventricular Shunting. Journal of Shaheed Suhrawardy Medical College, 17(1), 107-110. https://doi.org/10.3329/jssmc.v17i1.92343

Issue

Section

Case Reports

How to Cite

Saumitra Sarkar, Shuvro Saha, Saumik Sarkar, Md Shahadat Hossain Sarker, Avijit Dey, & Anindya Das Gupta. (2026). Dandy–Walker Malformation Presenting with Refractory Seizures and Unilateral Pan-ophthalmitis in Infancy: Successful Management with Dual Ventricular Shunting. Journal of Shaheed Suhrawardy Medical College, 17(1), 107-110. https://doi.org/10.3329/jssmc.v17i1.92343