Systemic Mastocytosis With Features of Chronic Liver Disease, Proptosis and Itchy Hyper-Pigmented Skin Lesion

Authors

  • - Md Benzamin Resident, Department of Pediatric Gastroenterology and Nutrition, Bangabandhu Sheikh Mujib Medical University, Dhaka, Bangladesh
  • Md Rafiqul Islam Resident, Department of Pediatric Gastroenterology and Nutrition, Bangabandhu Sheikh Mujib Medical University, Dhaka, Bangladesh
  • Mukesh Khadga Resident, Department of Pediatric Gastroenterology and Nutrition, Bangabandhu Sheikh Mujib Medical University, Dhaka, Bangladesh
  • Fahmida Begum Assistant Professor, Department of Pediatric Gastroenterology and Nutrition, Bangabandhu Sheikh Mujib Medical University, Dhaka, Bangladesh
  • Wahiduzzaman Mazumder Associate Professor, Department of Pediatric Gastroenterology and Nutrition, Bangabandhu Sheikh Mujib Medical University, Dhaka, Bangladesh
  • Shashi Bhushan Thakur Resident, Department of Pediatric Gastroenterology and Nutrition, Bangabandhu Sheikh Mujib Medical University, Dhaka, Bangladesh
  • Md Mahmudul Hasan FCPS student, Department of Pediatric Gastroenterology and Nutrition, Bangabandhu Sheikh Mujib Medical University, Dhaka, Bangladesh
  • ASM Bazlul Karim Professor, Department of Pediatric Gastroenterology and Nutrition, Bangabandhu Sheikh Mujib Medical University, Dhaka, Bangladesh

DOI:

https://doi.org/10.3329/kyamcj.v11i1.47152

Keywords:

Mastocytosis, Mast cells, Proptosis, Chronic Liver Disease

Abstract

Mastocytosisis a rare disorder of functionally defective mast cells. Infiltration of this functionally defective mast cells and CD34+ mast cell precursors in various organ leads to clinical manifestation. Skin is the most common affected organ. In systemic mastocytosis along with skin, internal organs such as the liver, spleen, bone marrow, small intestines and eye also involve. Diagnosis is done on the basis of WHO diagnostic criteria. Here we presenting this rare entity presented to us with features of chronic liver disease, proptosis and itchy hyperpigmented skin lesion diagnosed as systemic mastocytosis.

KYAMC Journal Vol. 11, No.-1, April 2020, Page 50-53

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Published

2020-05-17

How to Cite

Md Benzamin, .-., Islam, M. R., Khadga, M., Begum, F., Mazumder, W., Thakur, S. B., Hasan, M. M., & Karim, A. B. (2020). Systemic Mastocytosis With Features of Chronic Liver Disease, Proptosis and Itchy Hyper-Pigmented Skin Lesion. KYAMC Journal, 11(1), 50–53. https://doi.org/10.3329/kyamcj.v11i1.47152

Issue

Vol. 11 No. 1 (2020)

Section

Case Reports