Renal Primitive Neuroectodermal Tumor or Renal Ewing Sarcoma

Authors

  • Shakila Jannat Assistant Professor, Department of Pathology, Khwaja Yunus Ali Medical College and Hospital, Enayetpur, Sirajganj, Bangladesh
  • Halima Khatun Doly Assistant Professor, Department of Pathology, Khwaja Yunus Ali Medical College and Hospital, Enayetpur, Sirajganj, Bangladesh
  • Sayeed Bin Sharif Associate Professor, Department of Surgery, Khwaja Yunus Ali Medical College and Hospital, Enayetpur, Sirajganj, Bangladesh
  • Md Atiqur Rahman Professor, Department of Pathology, Khwaja Yunus Ali Medical College and Hospital, Enayetpur, Sirajganj, Bangladesh
  • A S M Akramul Islam Professor, Department of Pathology, Khwaja Yunus Ali Medical College and Hospital, Enayetpur, Sirajganj, Bangladesh

DOI:

https://doi.org/10.3329/kyamcj.v13i4.65086

Keywords:

Ewing sarcoma family tumors, Extraskeletal Ewing sarcoma, Renal Ewing sarcoma, Renal primitive neuroectodermal tumor (Renal PNET)

Abstract

Renal primitive neuroectodermal tumor (renal PNET) or renal Ewing sarcoma (renal ES) is a rare, rapidly growing malignant small round cell tumor with poor prognosis. A 32-years-old Bangladeshi male patient presented with right loin pain, fever and anemia. On CT imaging a large (18x10.5x10.0 cm) renal mass was discovered. On suspicion of malignancy, a biopsy was taken from the mass. Microscopic evaluation showed features consistent with malignant small round blue cell tumor. Immunohistochemical stains showed diffuse and strong positive reaction to CD-99 and negative for WT-1, CD-3 and CD-20, which confirmed the diagnosis of renal PNET. After 6 cycles of combined chemotherapy, the patient was relatively well and at 6 months follow-up he showed no evidence of metastasis or recurrence.

KYAMC Journal Vol. 13, No. 04, January 2023: 257-260

Downloads

Download data is not yet available.
Abstract
55
PDF
66

Downloads

Published

2023-03-30

How to Cite

Shakila Jannat, Halima Khatun Doly, Sayeed Bin Sharif, Md Atiqur Rahman, & A S M Akramul Islam. (2023). Renal Primitive Neuroectodermal Tumor or Renal Ewing Sarcoma . KYAMC Journal, 13(4), 257–260. https://doi.org/10.3329/kyamcj.v13i4.65086

Issue

Vol. 13 No. 4 (2023)

Section

Case Reports

License

Copyright (c) 2023 KYAMC Journal

Creative Commons License

This work is licensed under a Creative Commons Attribution 4.0 International License.